Primary primitive neuroectodermal tumor of the urinary bladder: A rare case report and review of literature

We report a rare case of primary primitive neuroectodermal tumor (PNET) of the urinary bladder. Primary PNETs of the bladder are very aggressive neoplasms. They are extremely rare and only few cases have been reported in the literature. A 26-year-old female patient who presented to us after excision biopsy is reported here. Initial histopathology examination report said the case to be small cell variant of malignant mesothelioma. Review and immunohistochemistry report confirmed the case as urinary bladder small round cell tumor with tumor cells expressing MIC-2. After excision of the tumor, bladder cystoscopy reveals normal study and patient is undergoing chemotherapy now.