Frantz's Tumor an Unusual Pancreatic Neoplasm with Rare Presentation

A solid pseudopapillary tumor of the pancreas (SPT) is alternatively called a 'Frantz tumor.' It was first named after its discoverer in the year 1959. This tumor has been previously designated as papillary epithelial neoplasm, low-grade papillary neoplasm, and solid and papillary neoplasm of the pancreas. It is a rare pancreatic neoplasm. It typically affects young people and has a female predilection. Its histogenesis is rather debatable. Acinar, endocrine, ductal, and progenitor cells have been postulated as a possible starting point of this tumor. It has a relatively favorable prognosis with low malignant potential. It accounts for less than 3% of all exocrine pancreatic neoplasms. Although most SPTs behave as benign tumors, up to 15% of the cases can show malignancy. We are presenting a rare case of a 19-year-old female who came with epigastric abdominal pain. Surgical excision was done, and a histopathology/Immunohistochemistry examination confirmed it as a Frantz tumor.