TY  - JOUR
T1  - Peutz-Jegher′s syndrome with gut maltoma: A rare presentation
A1  - Anindya Mukherjee
A1  - Subrata Chattopadhyay
A1  - Md. Azam
A1  - Aramita Saha
JF  - Clinical Cancer Investigation Journal
JO  - Clin Cancer Investig J
SN  - 2278-0513
Y1  - 2014
VL  - 3
IS  - 4
DO  - 10.4103/2278-0513.134509
SP  - 350
EP  - 352
N2  - Peutz-Jegher′s syndrome (PJS) is an autosomal dominant disorder characterized by numerous hamartomatous polyps in the gastrointestinal tract (GIT) and pigmented muco-cutaneous lesions. We present here a case of a maltoma associated with multiple hamartomatous polyps detected in a post-operative ileocolic specimen of a 28-year-old man. Prior to this, he had undergone surgery for intussusception when similar polyps were noted in the small bowel. Upper GIT endoscopy also confirmed the diffuse presence of such polyps. A clinico-pathological diagnosis of PJS was made, which by itself is rarely encountered. Furthermore, the detection of mucosa associated lymphoid tissue lymphoma/maltoma in a background of PJS is remarkably unique in this case, for which it has been reported.
UR  - https://ccij-online.org/article/peutz-jegher′s-syndrome-with-gut-maltoma:-a-rare-presentation-242
ER  -