%0 Journal Article
%T Orbito-cranial mesenchymal chondrosarcoma in a young female: A rare case report
%A Shyam Sharma
%A Somnath Roy
%A Imraan Khan
%A Suparna Pal
%A Anup Majumdar
%J Clinical Cancer Investigation Journal
%@ 2278-0513
%D 2015
%V 4
%N 3
%R 10.4103/2278-0513.151941
%P 416-418
%X Mesenchymal chondrosarcoma (MCS) of the head and neck is highly aggressive malignant small round cell neoplasm with cartilaginous differentiation, often with a pericytomatous vascular pattern. It represents approximately 0.1% of all head and neck neoplasms. Chondrosarcoma of orbit is extremely rare. We report a case of orbito-cranial MCS in a 24-year-old female who presented with exophthalmos. Imaging revealed a large heterogenous lesion arising from right orbit with intracranial extension. Patient underwent right fronto-temporal craniotomy with tumor decompression from intracranial part and right orbit. Histopathologic examination and immunohistochemistry was suggestive of MCS. Postoperative residual disease was treated with chemotherapy showing partial response.
%U https://ccij-online.org/article/orbito-cranial-mesenchymal-chondrosarcoma-in-a-young-female:-a-rare-case-report-409